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HelpTest Code PIPA Pipecolic Acid, Serum
Necessary Information
Patient's age is required.
Specimen Required
Patient Preparation: Fasting 12 hours or more. (Collect specimens from infants and small children just before next feeding)
Supplies: Sarstedt Aliquot Tube, 5 mL (T914)
Collection Container/Tube:
Preferred: Serum gel
Acceptable: Red top
Submission Container/Tube: Plastic vial
Specimen Volume: 1.5 mL
Collection Instructions: Centrifuge and aliquot serum into plastic vial.
CMH COLLECTION: 3 mL in red gel vacutainer
Specimen Minimum Volume
1 mL
Specimen Stability Information
| Specimen Type | Temperature | Time | Special Container |
|---|---|---|---|
| Serum | Frozen (preferred) | 94 days | |
| Refrigerated | 14 days |
Testing Algorithm
For more information see Epilepsy: Unexplained Refractory and/or Familial Testing Algorithm
Useful For
Differentiating between disorders of peroxisomal biogenesis (eg, Zellweger syndrome) and disorders with loss of a single peroxisomal function
Detecting abnormal elevations of pipecolic acid in serum
Reject Due To
| Gross hemolysis | OK |
| Gross lipemia | OK |
| Gross icterus | OK |
Day(s) Performed
Tuesday
Report Available
3 to 9 daysReporting Name
Pipecolic Acid, SReference Values
<6 months: ≤6.0 nmol/mL
6 months-<1 year: ≤5.9 nmol/mL
1-17 years: ≤4.3 nmol/mL
≥18 years: ≤7.4 nmol/mL
Method Name
Gas Chromatography Mass Spectrometry (GC-MS)
Performing Laboratory
Mayo Clinic Laboratories in Rochester
CPT Code Information
82542