Prader-Willi Syndrome
Collection Requirements
Source: blood
Container: EDTA lavender
Volume:
- Preferred: 3 mL in vacutainer
- Minimum: 1 mL in vacutainer
Turn Around Time
14 days
Availability
Routine
Lab Processing Instructions
Specimen: whole blood
Room temperature or refrigerate
Performing Laboratory
Adele Hall
Adele Hall Lab Section
Molecular Genetics
Instrumentation/Methodology
MS-MLPA (methylation sensitive multiple ligation probe assay) is used to detect copy number changes and methylation status of Chromosome 15
Additional Information
Prader-Willi syndrome (PWS) is an imprinting disorder caused by abnormal imprinting or deletion of chromosomal region 15p11.2-q13 on the paternally-inherited chromosome. PWS is characterized by severe hypotonia and feeding difficulties in early infancy, followed in later childhood by excessive eating and gradual development of morbid obesity, unless externally controlled. Cognitive impairment, hypogonadism, short stature, and small hands and feet are common.
Reference Ranges
See interpretive report
CPT
81331